CAOPORN成人免费公开,欧美FREESEX黑人又粗又大 ,欧美狠狠入鲁的视频777色,主仆调教SM束缚绳索捆绑

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯(lián)系我們
亚洲人成在线观看,我的初次内射欧美成人影视,我是班主任在线观看免费
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-Fibrillin 2/BF647 Conjugated antibody (bs-12166R-BF647)
訂購熱線:400-901-9800
訂購郵箱:sales@www.tjshangbang.com
訂購QQ:  400-901-9800
技術支持:techsupport@www.tjshangbang.com
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-12166R-BF647
英文名稱 Rabbit Anti-Fibrillin 2/BF647 Conjugated antibody
中文名稱 BF647標記的原纖維蛋白2抗體
別    名 CCA; congenital contractural arachnodactyly (Marfanoid-like); DA9; FBN2; FBN2_HUMAN; fibrillin 2 (congenital contractural arachnodactyly); Fibrillin-2.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  神經(jīng)生物學  信號轉導  結合蛋白  細胞外基質  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep, )
產(chǎn)品應用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 311kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Fibrillin 2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Extracellular glycoproteins fibrillin-1 and -2 are major components of connective tissue microfibrils. Fibrillin-2 containing microfibrils regulate the early process of elastic fiber assembly in tissue. Mutations in the fibrillin-2 gene resulting in impaired assembly of fibrillin-2 may lead to molecular congenital contractural arachnodactyly. Fibrillin-2 constitutes the backbone of microfibrils which insert directly into the lamina densa of basement membranes. Epithelial cells primarily deposit fibrillin into the extracellular matrix in a nonfibrillar form. Mutations in the 8-cysteine motif of Fibrillin-2 alters its binding to microfibril-associated glycoprotein-1 (MAGP-1), which may increase the severity of congenital contractural arachnodactyly.

Function:
Fibrillins are structural components of 10-12 nm extracellular calcium-binding microfibrils, which occur either in association with elastin or in elastin-free bundles. Fibrillin-2-containing microfibrils regulate the early process of elastic fiber assembly. Regulates osteoblast maturation by controlling TGF-beta bioavailability and calibrating TGF-beta and BMP levels, respectively.

Subcellular Location:
Secreted

DISEASE:
Defects in FBN2 are the cause of congenital contractural arachnodactyly (CCA) [MIM:121050]; also known as Beals syndrome or distal arthrogryposis type 9 (DA9). CCA is a rare, autosomal dominant connective tissue disorder characterized by contractures, arachnodactyly, scoliosis, and crumpled ears. Phenotypically similar to Marfan syndrome, CCA does not affect the aorta and the eyes.

Similarity:
Belongs to the fibrillin family.
Contains 47 EGF-like domains.
Contains 9 TB (TGF-beta binding) domains.

Database links:

Entrez Gene: 2201 Human

Entrez Gene: 100047082 Mouse

Entrez Gene: 14119 Mouse

Entrez Gene: 689008 Rat

Omim: 121050 Human

SwissProt: P35556 Human

SwissProt: Q61555 Mouse

Unigene: 519294 Human

Unigene: 20271 Mouse

Unigene: 22906 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 www.www.tjshangbang.com 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
双性美人受哭酸深捣H| 国产一区二区在线观看免费观看| 日本三级片在线观看| 人妻中文字幕精品一页| 久久青青草原精品国产 | 伊人春色xxhd| 亚洲A∨精品无码一区二区| 人妻少妇精品无码专区二区| 蜜桃AV蜜臀AV色欲AV| 毛片男女啪啪内射无遮挡| 日本一区二区在线播放| 在丈前下药侵犯人妻在线| 婷婷色婷婷开心五月四房播播| 亚洲欧美日韩中文字幕在线| 91午夜精品亚洲一区二区三区| 耻辱の中出し授业大桥未久| 美女视频免费是黄的网站| 男男无遮挡H肉真人在线观看| 99久久国产宗和精品1上映| 少妇一晚三次一区二区三区| 午夜视频在线观看一区| 农村人乱弄一区二区的处罚方式| 一二三四社区在线视频观看| 免费香蕉视频国产在线看| 精品人人妻人人澡人人爽牛牛| 亚洲精品国产精品国自产观看| 四虎国产精品成人免费久久| 真实国产乱子伦视频| 国产AV午夜精品一区二区入口| 99RE久久精品国产| 国产成人无码午夜视频在线观看| 韩国午夜理伦三级好看2020| 美人被强行糟蹋NP 各种PLAY| 久久国产精品久久久久久电车| 韩国午夜理伦三级好看2020| 与亲女洗澡时伦了毛片| 亚洲专区国产精品欧美电影| 日韩欧美一区久久| 日韩精品中文字幕少妇| 午夜亚洲福利在线老司机| 人妻无码中文专区久久AV|