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Rabbit Anti-ACADS  antibody (bs-23057R)
~~~促銷代碼KT202410~~~
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產品編號 bs-23057R
英文名稱 Rabbit Anti-ACADS  antibody
中文名稱 ?;o酶A脫氫酶短鏈抗體
別    名 ACAD3; Acyl Coenzyme A dehydrogenase, C2 to C3 short chain; Acyl-CoA dehydrogenase, C2 to C3 short chain; Acyl-CoA dehydrogenase, short chain; Acyl-Coenzyme A dehydrogenase, short chain; AI196007; Bcd-1; Bcd1; Butyryl CoA dehydrogenase; EC 1.3.99.2; SCAD; Short chain acyl CoA dehydrogenase; Short-chain specific acyl-CoA dehydrogenase, mitochondrial; Unsaturated acyl CoA reductase; ACADS_HUMAN.  
研究領域 腫瘤  細胞生物  免疫學  轉錄調節(jié)因子  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human,Mouse,Rat,Pig,Cow)
產品應用 WB=1:500-2000
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
理論分子量 45kDa
細胞定位 細胞漿 線粒體
性    狀 Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ACADS: 121-220/412 
亞    型 IgG
純化方法 affinity purified by Protein A
緩 沖 液 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
保存條件 Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles.
注意事項 This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
PubMed PubMed
產品介紹 ACADS is a homotetramer mitochondrial flavoprotein, which is a member of the acyl CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. Mutations in this gene have been associated with Short Chain Acyl CoA Dehydrogenase Deficiency.

Subcellular Location:
Mitochondrion matrix.

DISEASE:
Defects in ACADS are the cause of acyl-CoA dehydrogenase short-chain deficiency (ACADSD) [MIM:201470]. It is an autosomal recessive disorder resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults.

Similarity:
Belongs to the acyl-CoA dehydrogenase family.

SWISS:
P16219

Gene ID:
35

Database links:

Entrez Gene: 35 Human

Entrez Gene: 11409 Mouse

Entrez Gene: 64304 Rat

Omim: 606885 Human

SwissProt: P16219 Human

SwissProt: Q07417 Mouse

SwissProt: P15651 Rat

Unigene: 507076 Human

Unigene: 18759 Mouse

Unigene: 1167 Rat



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